СЕРПОВИДНО-КЛЕТОЧНАЯ АНЕМИЯ (HBSS) У ВЗРОСЛОГО БОЛЬНОГО ИЗ ТАНЗАНИИ

SICKLE-CELL ANEMIA (HBSS) IN AN ADULT PATIENT FROM TANZANIA

There is a description of an observation of patient N., aged 29, (a student of Russian University for Peoples' Friendship and a citi­zen of Tanzania) suffering from sickle-cell anemia - SCA — (Hb-SS), homozygous type, which was detected at screening of abnor­mal Hb by electrophoresis on the cellulose acetate strips. The re­sults of clinical-and-biological examinations of the patients are de­scribed. The patient had anemia (Hb 98-83 g/L); thrombotic (pain) crises with dark urination were periodically observed. HbS account­ed for the bulwark (98%) of Hb, while small fractions of Hb (HbF and HbA ₂) were within the normal limits. This was a comparatively mild form of the disease; the patient had minor changes in the heart and lungs with other internal bodies being intact. Patient N. received, from childhood, an appropriate therapy including antibi­otics, folic acid, analgesics etc. Obviously, this provides for an ex­planation to that he lived up to 29 years, withstood the acclimatiza­tion in Russia and could get education. A comparison of the clini-cal-and-laboratory indices of patient N. with the data of patients with SCA of other types (HbS-thalassemia, HbSC and HbSK) is presented.