Skin mast cells in Marfan syndrome: specific emphasis on connective tissue remodeling

[No abstract available]

Авторы
Atiakshin D. , Nikolaeva E. , Gritsevskaya D. , Semyachkina A. , Kostin A. , Volodkin A. , Morozov S. , Dlin V. , Ignatyuk M. , Mikhaleva L. , Elieh-Ali-Komi D. , Buchwalow I. , Tiemann M.
Издательство
Springer Verlag
Номер выпуска
6
Язык
Английский
Статус
Опубликовано
Номер
271
Том
316
Год
2024
Организации
  • 1 RUDN University, 6 Miklukho-Maklaya St, Moscow, 117198, Russian Federation
  • 2 Veltischev Research and Clinical Institute for Pediatrics & amp
  • 3 Pediatric Surgery of the Pirogov, Russian National Research Medical University, 2, Taldomskaya St, Moscow, 125412, Russian Federation
  • 4 Research Institute of Experimental Biology and Medicine, Burdenko Voronezh State Medical University, Voronezh, Russian Federation
  • 5 Avtsyn Research Institute of Human Morphology, Petrovsky National Research Center of Surgery, Moscow, 119435, Russian Federation
  • 6 Institute of Allergology, Corporate Member of Freie, Charité - Universitätsmedizin Berlin, Universität Berlin and Humboldt-Universität zu Berlin, Berlin, Germany
  • 7 Allergology and Immunology, Fraunhofer Institute for Translational Medicine and Pharmacology ITMP, Berlin, Germany
  • 8 Institute for Hematopathology, Fangdieckstr. 75a, Hamburg, 22547, Germany
Ключевые слова
Connective Tissue; Fibrillin-1; Humans; Marfan Syndrome; Mast Cells; Skin; fibrillin 1; proteinase; stem cell factor receptor; fibrillin 1; collagen fibril; connective tissue; elastic fiber; fibroblast; histochemistry; human; immunohistochemistry; Letter; Marfan syndrome; mast cell; protein expression; secretory granule; skin; skin cell; stroma cell; connective tissue; diagnosis; genetics; immunology; metabolism; pathology
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