Infantile cranial fasciitis

Cranial fasciitis (CF) is a rare benign lesion of the skull. Due to the rarity of this disease, prospective studies of it have not been conducted. The first description dedicated of the case of CF was in 1980. Later were descriptions of only clinical cases of observation and treatment of children with this pathology. For these reasons, questions regarding true incidence, genetic risk factors, prognosis and long-term still unanswered. Clinically, CF is represented by a dense, painless, growing mass on the scalp. Given the rarity of the occurrence of CF in differential diagnosis, it is usually not considered. In addition, there are no pathognomonic clinical signs and symptoms, and changes on MRI are often non-specific. Treatment involves removal of the tumor mass, after which a histopathological examination confirms the diagnosis of CF. As a rule, a good result is observed with complete resection, however, in this case it has to necessary to perform auto-bone grafting of the skull bone defect. CF is a rare and underexplored fibroproliferative disease. Because of its locally invasive nature and nonspecific manifestations of CF, it is often difficult to distinguish from malignant neoplasms and infections. Complete surgical removal is the best choice to make diagnosis and successful treatment. Parents gave their consent to use information about the child in the article. © 2019 by NMRC PHOI.

Publisher
Фонд поддержки и развития в области детской гематологии, онкологии и иммунологии Врачи, инновации, наука - детям
Number of issue
4
Language
Russian
Pages
66-78
Status
Published
Volume
18
Year
2019
Organizations
  • 1 Peoples' Friendship University of Russia, Moscow, Russian Federation
  • 2 Russian Children's Clinical Hospital of the Pirogov Russian National Research Medical University of the Ministry of Healthcare of the Russian Federation, Moscow, Russian Federation
Keywords
Cranial; Cranialfasciitis; Fasciitis; Fibroproliferative; Infantile; Primary skull lesion
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