A Case Report of Al-Amyloidosis with «Hepatic Disguise» of Nephrotic Syndrome; [КЛИНИЧЕСКИЙ СЛУЧАЙ AL-АМИЛОИДОЗА С ПОРАЖЕНИЕМ ПЕЧЕНИ И РАЗВИТИЕМ НЕФРОТИЧЕСКОГО СИНДРОМА У МОЛОДОЙ ЖЕНЩИНЫ]

Amyloidosis is characterized by damage to several organ systems, which leads to diagnostic delays and progression of the pathological process. The described clinical case demonstrates a long diagnostic search in a patient with AL-amyloidosis. According to the literature, the most often described manifestation of the disease is kidney damage that manifests as nephrotic syndrome. This case is interesting because the reason for hospitalization was liver damage. Laboratory tests revealed cholestatic and cytolytic syndromes and dyslipidemia. Differential diagnostic included diseases with liver damage. In the hospital nephrotic syndrome was identified, renal biopsy was performed that proved the diagnosis of AL-amyloidosis with combined damage to the gastrointestinal tract, liver and kidneys. © 2024 SINAPS LLC. All rights reserved.

Авторы
Kozlova A.A. , Rauzheva V.P. , Yunyaev A.R. , Mayorov V.V. , Manyakina E.V. , Kokorin V.A. , Stolyarevich E.S. , Poteshkina N.G.
Номер выпуска
3
Язык
Русский
Страницы
206-212
Статус
Опубликовано
Том
14
Год
2024
Организации
  • 1 Pirogov Russian National Research Medical University, P. E. Lukomsky Department of Hospital Therapy of Medicine Faculty, Moscow, Russian Federation
  • 2 Municipal Clinical Hospital № 15, Moscow Healthcare Department, Moscow, Russian Federation
  • 3 Peoples' Friendship University of Russia named after Patrice Lumumba, Department of Hospital Therapy with courses in Endocrinology, Hematology and Clinical Laboratory Diagnostics, Moscow, Russian Federation
  • 4 A.I. Yevdokimov Moscow State University of Medicine and Dentistry, Department of Nephrology, Faculty of Continuing Professional Education, Moscow, Russian Federation
  • 5 City Clinical Hospital № 52, Moscow Healthcare Department, Moscow, Russian Federation
  • 6 Pirogov Russian National Research Medical University, Department of General Therapy, Faculty of Continuing Professional Education, Moscow, Russian Federation
Ключевые слова
AL-amyloidosis; nephrotic syndrome; renal biopsy
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