Acute myocardial infarction-like event in a young patient with biventricular arrhythmogenic cardiomyopathy; [Бивентрикулярная аритмогенная кардиомиопатия под маской инфаркта миокарда у пациента молодого возраста]

The article describes a clinical case of biventricular arrhythmogenic cardiomyopathy (ACM) presented with myocardial infarction (MI) - like event in a young patient. The patient was hospitalized with suspected acute coronary syndrome and an episode of ventricular tachycardia (VT). Based on increased cardiac troponin, left ventricular systolic dysfunction with wall motion abnormalities, and nonobstructive coronary arteries the initial diagnosis of type 2 MI was made. To verify the etiology behind VT and ventricular structural abnormalities cardiac magnetic resonance imaging (MRI) was performed. Abnormalities of both right and left ventricles demonstrated by MRI and supported by the genetic testing established the diagnosis of biventricular ACM. Since the diagnosis was made, initially diagnosed MI was reassessed in favor of acute myocardial injury as a characteristic of ACM course. ACM should be included into differential diagnosis with MI and acute myocarditis in patients with elevated troponin and nonobstructive coronary arteries. © 2024 Stolichnaya Izdatelskaya Kompaniya. All rights reserved.

Авторы
Stavtseva Y.V. , Mershina E.A. , Lobzhanidze T.V. , Bazdyreva E.I. , Khutsishvili N.I. , Kobalava Z.D.
Издательство
Stolichnaya Izdatelskaya Kompaniya
Номер выпуска
1
Язык
Русский
Страницы
57-62
Статус
Опубликовано
Том
20
Год
2024
Организации
  • 1 RUDN University, Moscow, Russian Federation
  • 2 Lomonosov Moscow State University, Moscow, Russian Federation
Ключевые слова
acute myocardial injury; arrhythmogenic cardiomyopathy; myocardial infarction; troponin I; ventricular tachycardia
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