The structure of interstitial lung diseases in children of the first two years of life

For the first time in Russia, the article provides data on interstitial lung diseases structure in children of the first two years of life, based on a series of observations of 68 patients with these rare diseases, as a part of multi-center ambispective study. Interstitial lung diseases in observed children included: Wilson-Mikity syndrome (23,4%), neuroendocrine hyperplasia of infancy (22%), bronchiolitis obliterans with organizing pneumonia (7,4%), primary pulmonary hypoplasia (1,5%), secondary pulmonary hypoplasia with Jeune syndrome (10,3%), secondary pulmonary hypoplasia with Edwards syndrome (2,9%), secondary pulmonary hypoplasia with other associated pathology (omphalocele - 1,5%, non-immune fetal hydrops - 1,5%), subpleural cysts in patients with Down syndrome (5,9%), congenital deficiency of surfactant protein B (1,5%), brain-lung- thyroid syndrome (2,9%), congenital alveolar-capillary dysplasia (1,5%), interstitial lung diseases with systemic diseases (Langerhans cell histiocytosis - 16,2%, Niemann-Pick disease - 1,5%). The article summarizes clinical features, the results of image diagnosis and disease outcomes. © 2015, Pediatria Ltd. All rights reserved.

Authors
Ovsyannikov D.Y. 1, 2, 3 , Belyashova M.A. 1 , Boytsova E.V.4 , Avakyan A.A. 3 , Alekseeva O.V. 1 , Asherova I.K.5 , Asherova-Yushkova D.V.6 , Bogdanova A.V.4 , Bolibok A.M. 1, 3 , Bronin G.O.2 , Valtts N.L.2 , Vlasova A.V.6 , Volkov S.N.7 , Volkova I.E.6 , Gitinov S.A. 1 , Glazyrina A.A.2 , Goloborodko M.M.8 , Gorbunov A.V.2, 9 , Grishkevich N.L.2 , Degtyareva E.A. 1, 3 , Donin I.M.2 , Esipenko A.P.6 , Zhakota D.A.9 , Zhdanova O.I. 3 , Zaytseva N.O.3 , Zaytseva S.V.10 , Zapevalova E.J.4 , Zaharova L.A.3 , Ivanova N.N.11 , Illarionova T.Y. 1 , Koltunov I.E. 1, 2 , Kondratchik K.L.2 , Korsunskiy A.A.12 , Krushelnitskiy A.A. 1, 3 , Krushelnitskiy A.A. 1, 3 , Kustova O.V.13 , Malinina O.V.16 , Marchenkov Y.V.14 , Nazarova T.I. 1 , Narogan M.V.15 , Pavlova E.S.3 , Petruk N.I. 1, 3 , Petryaykina E.E. 1, 2 , Postnikova E.V.16 , Pugacheva I.A.2 , Pushkareva J.E.17 , Pushko L.V. 1 , Rogatkin P.S.2 , Samsonovich I.R.2 , Semenova L.P.2 , Starevskaya S.V.8 , Stepanov O.G. 17 , Stepanova E.V. 1 , Suryaninova O.V.6 , Suslova O.V.7 , Turina I.E.18 , Usacheva O.V.5 , Fedorov I.A.17 , Fedotova O.P.5 , Feldfiks L.I.12 , Hromova A.V.2 , Chernyaev A.P.19 , Chusov K.P.2 , Sholtoyanu A.V.3 , Shokin A.A.2, 3
Journal
Pediatriya - Zhurnal im G.N. Speranskogo
Number of issue
1
Language
Russian
Pages
72-81
Status
Published
Link
External link
Volume
95
Year
2016
Organizations
  • 1 People’s Friendship University of Russia, Russian Federation
  • 2 Morozov Children’s City Clinical Hospital, Moscow, Russian Federation
  • 3 Children’s Infectious Diseases Clinical Hospital No 6, Moscow, Russian Federation
  • 4 Scientific Research Institute of Pulmonology, Pavlov First Saint Petersburg State Medical University, Russian Federation
  • 5 Children’s Clinical Hospital No 1, Yaroslavl, Russian Federation
  • 6 Regional Children’s Hospital, Yaroslavl, Russian Federation
  • 7 Perinatal Medical Center, Moscow, Russian Federation
  • 8 Rauhfus Children’s City Hospital No 19, Russian Federation
  • 9 Pirogov Russian National Research Medical University, Moscow, Russian Federation
  • 10 Moscow State University of Medicine and Dentistry named after A.I. Evdokimov, Russian Federation
  • 11 Yaroslavl State Medical University, Yaroslavl, Russian Federation
  • 12 Children Clinical Hospital No 9 named after G.N. Speransky, Russian Federation
  • 13 Scientific Center of Children’s Health, Moscow, Russian Federation
  • 14 Consultative and Diagnostic Center MEDSI, Moscow, Russian Federation
  • 15 Research Center for Obstetrics, Gynecology and Perinatology named after V.I. Kulakov, Russian Federation
  • 16 Scientific-Practical Center of Medical Care for Children with Craniofacial Developmental Disabilities and Congenital Diseases of the Nervous System, Moscow, Russian Federation
  • 17 South Ural State Medical University, Chelyabinsk, Russian Federation
  • 18 I.M. Sechenov First Moscow State Medical University, Moscow, Russian Federation
  • 19 Scientific Research Institute of Pulmonology, Federal Biomedical Agency, Moscow, Russian Federation
Keywords
Children; Computed tomography diagnostics; Interstitial lung diseases
Date of creation
19.10.2018
Date of change
13.07.2022
Short link
https://repository.rudn.ru/en/records/article/record/4466/
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